HIBCH — 카탈로그 13건
Gene HIBCH
NCBI Gene 26275
취급 제조사 4곳
국내 소싱 가능
13건
유전자 개요
이 유전자는 HIBYL-CoA와 beta-hydroxypropionyl-CoA 모두의 가수분해(hydrolysis)를 담당하는 효소(enzyme)를 암호화한다. 이 유전자의 변이는 3-hydroxyisobutyryl-CoA 가수분해효소 결핍과 관련이 있다. 대체 스플라이싱(splicing)은 여러 전사체 변이체를 생성한다.
3-hydroxyisobutyryl-CoA hydrolase deficiencyBranched-chain amino acid catabolism
3-hydroxyisobutyryl-CoA hydrolase deficiencyNeurodegeneration due to 3-hydroxyisobutyryl-CoA hydrolase deficiencygenetic disorderneurodegenerative diseasemethylmalonate (MMA) measurementlevel of 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial in blood serumglomerular filtration rateprotein measurement
데이터 출처 · 근거
- NCBI Gene ↗유전자 정보
- Open Targets ↗질환 연관·생물학적 경로
체크박스로 여러 제품을 선택해 한 번에 견적을 요청하세요. 제조사·Cat No·Application을 한 표에서 비교합니다.
| 견적 | 제조사 | Cat No | Mfr No | 제품명 | Host | Clonality | Reactivity | Application | Size |
|---|---|---|---|---|---|---|---|---|---|
| Biosynth | F502-104669-01 | 10R-4352 | HIBCH antibody | Mouse | Monoclonal | Human; Cross: Human, Dog, Rat | FC, IF, WB | 100 ul | |
| Biosynth | F502-120711-01 | 70R-17735 | HIBCH antibody | Rabbit | Polyclonal | Human; Cross: Human, Mouse, Rat | ELISA, IHC, WB | 50 ul | |
| Biosynth | F502-104671-01 | 10R-4358 | HIBCH antibody | Mouse | Monoclonal | Human; Cross: Human, Dog, Rat | FC, IF, WB | 100 ul | |
| Biosynth | F502-104667-01 | 10R-4350 | HIBCH antibody | Mouse | Monoclonal | Human; Cross: Human, Dog | FC, IHC | 100 ul | |
| Biosynth | F502-104668-01 | 10R-4351 | HIBCH antibody | Mouse | Monoclonal | Human; Cross: Human | FC, IF, WB | 100 ul | |
| Biosynth | F502-104666-01 | 10R-4349 | HIBCH antibody | Mouse | Monoclonal | Human; Cross: Human | FC, IF, WB | 100 ul | |
| Biosynth | F502-104670-01 | 10R-4357 | HIBCH antibody | Mouse | Monoclonal | Human; Cross: Human | FC, IF, WB | 100 ul | |
| Cloud-Clone | T813-125275-01 | PAD683Mu01 | Polyclonal Antibody to 3-Hydroxyisobutyryl Coenzyme A Hydrolase (HIBCH) | Rabbit | Polyclonal | Murine | WB | 100µl |
관련 표적
같은 생물학적 경로를 공유하는 표적 — 함께 검토되는 시약군입니다.
BCAT1
Branched-chain amino acid catabolism
BCKDK
Branched-chain amino acid catabolism
ACADSB
Branched-chain amino acid catabolism
DLD
Branched-chain amino acid catabolism
MCCC2
Branched-chain amino acid catabolism
HSD17B10
Branched-chain amino acid catabolism
BCAT2
Branched-chain amino acid catabolism
ACAT1
Branched-chain amino acid catabolism