해외 연구시약 수입·전문 취급 · 국내 대리점 관련 문의

GLA — 카탈로그 36건

Gene GLA NCBI Gene 2717
국내 소싱 가능
36건

유전자 개요

GLA 유전자는 해당 효소가 당지질과 당단백질에서 말단의 알파-갈라토실 잔기를 가수분해하는 데 필요합니다. 이 효소는 주로 세라마이드 트리헥소사이드를 가수분해하며, 멜리비오스를 갈락토스와 포도당으로 가수분해하는 것을 촉매할 수 있습니다. 이 유전자의 다양한 돌연변이는 효소의 합성, 가공, 안정성에 영향을 미쳐, 알파-D-갈락토실 당지질 잔기의 분해 실패로 발생하는 희귀 리소좀 저장 질환인 파브리병을 유발합니다.

Glycosphingolipid catabolismNeutrophil degranulation
Fabry diseasecardiomyopathyAngiokeratoma corporis diffusumAbnormality of the cardiovascular systemtrait in response to migalastathypertrophic cardiomyopathyRenal insufficiencyfamilial hypertrophic cardiomyopathy
데이터 출처 · 근거

체크박스로 여러 제품을 선택해 한 번에 견적을 요청하세요. 제조사·Cat No·Application을 한 표에서 비교합니다.

견적제조사Cat NoMfr No제품명HostClonalityReactivityApplicationSize
CusabioT094-110250-01CSB-RA950991A0HUGLA Recombinant Monoclonal AntibodyRabbitMonoclonalHumanELISA, IHC, FC50μl, 100μl
Cloud-CloneT813-107837-01LAA183Hu82FITC-Linked Monoclonal Antibody to Galactosidase Alpha (GLa)MouseAntibody labelingHumanWB; IHC; ICC; IF.100µl
Cloud-CloneT813-107836-01LAA183Hu81FITC-Linked Polyclonal Antibody to Galactosidase Alpha (GLa)RabbitAntibody labelingHumanWB; IHC; ICC; IF.100µl
MyBioSourceR247-189501-01MBS8106153GLA/alpha-Galactosidase A, Monoclonal AntibodyMouseMonoclonalHumanWB; ELISA; Cap0.02 mL
MyBioSourceR247-189500-01MBS8106152GLA/alpha-Galactosidase A, Monoclonal AntibodyMouseMonoclonalHumanELISA0.1 mL
MyBioSourceR247-132617-01MBS2115171Galactosidase Alpha (GLa), Polyclonal AntibodyRabbitPolyclonalHumanWB; IHC; Immunocytochemistry (ICC).0.1 mL
BiosynthF502-120446-0170R-17490GLA antibodyRabbitPolyclonalHuman; Cross: Human, Mouse, RatELISA, IHC, WB50 ul
Cloud-CloneT813-117595-01PAA183Hu03Polyclonal Antibody to Galactosidase Alpha (GLa)RabbitPolyclonalHumanIHC; ICC/IF100µl
Cloud-CloneT813-111640-01MAA183Hu22Monoclonal Antibody to Galactosidase Alpha (GLa)MouseMonoclonalHumanWB; IHC100µl
Cloud-CloneT813-117593-01PAA183Hu01Polyclonal Antibody to Galactosidase Alpha (GLa)RabbitPolyclonalHumanIHC; FCM100µl
Cloud-CloneT813-128891-01PSA183Hu01Antibody Pair for Galactosidase Alpha (GLa)RabbitPolyclonalHumanELISA; CLIA; ELISPOT; Luminex; Immunochromatography and other Immunoassays.96T*10
Cloud-CloneT813-117594-01PAA183Hu02Polyclonal Antibody to Galactosidase Alpha (GLa)RabbitPolyclonalHumanWB,IHC,ICC/IF,FCM100µl
Cloud-CloneT813-117596-01PAA183Mu01Polyclonal Antibody to Galactosidase Alpha (GLa)RabbitPolyclonalMurineWB; IHC; ICC; IP.100µl
Cloud-CloneT813-111639-01MAA183Hu21Monoclonal Antibody to Galactosidase Alpha (GLa)MouseMonoclonalHumanWB; IHC100µl
MyBioSourceR247-200952-01MBS9201838GLA, Polyclonal AntibodyRabbitPolyclonalHumanWB; ELISA; IHC; IF; FC/FACS0.08 mL
MyBioSourceR247-124901-01MBS2002841Galactosidase Alpha (GLa), Polyclonal AntibodyRabbitPolyclonalHumanWB; ICC; IHC; IP0.1 mL
MyBioSourceR247-125542-01MBS2007282Galactosidase Alpha (GLa), Polyclonal AntibodyRabbitPolyclonalHumanICC; Immunohistochemistry (IHC) - Formalin/Paraffin; ELISA; WB0.1 mL
MyBioSourceR247-123794-01MBS178636Gla, Polyclonal AntibodyRabbitPolyclonalMouseWB0.01 mg
BiosynthF502-136671-0170R-5451GLA antibodyRabbitPolyclonalHuman; Cross: Predicted: Human, Mouse, Rat, Cow, Dog, Goat, Guinea Pig, Horse, Rabbit, ZebrafishWB100 ul
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