해외 연구시약 수입·전문 취급 · 국내 대리점 관련 문의

DBT — 카탈로그 4건

Gene DBT NCBI Gene 1629
취급 제조사 3곳
국내 소싱 가능
4
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIVBranched-chain amino acid catabolismBranched-chain ketoacid dehydrogenase kinase deficiencyH139Hfs13* PPM1K causes a mild variant of MSUDLoss-of-function mutations in BCKDHA or BCKDHB cause MSUDLoss-of-function mutations in DBT cause MSUD2Loss-of-function mutations in DLD cause MSUD3/DLDDMitochondrial protein degradationProtein lipoylationRHOH GTPase cycle
maple syrup urine diseasemaple syrup urine disease type 1Aleucine measurementamino acid measurementvaline measurementisoleucine measurementmaple syrup urine disease type 2convulsion

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견적제조사Cat NoMfr No제품명HostClonalityReactivityApplicationSize
CusabioT094-105635-01CSB-PA006530LA01HUDBT AntibodyRabbitPolyclonalHuman, MouseELISA, WB50μg, 100μg
BiosynthF502-125410-0170R-2499DBT antibodyRabbitPolyclonalHuman; Cross: Predicted: Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse, Rabbit, Yeast, ZebrafishWB100 ul
BiosynthF502-119641-0170R-16751DBT antibodyRabbitPolyclonalHuman; Cross: Human, Mouse, RatELISA, WB50 ul
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